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Antibody

Anti-Dysferlin (DYSF) Antibody

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DESCRIPCIÓN

Supplier:Huabio
Reference:ER1511-12
Name:Anti-Dysferlin (DYSF) Antibody
Category:Antibody
Subcategory:Primary antibodies
Aditional Names:DMAT antibody DYSF antibody DYSF_HUMAN antibody Dysferlin antibody Dysferlin limb girdle muscular dystrophy 2B (autosomal recessive) antibody Dysferlin limb girdle muscular dystrophy 2B antibody Dystrophy associated fer 1 like 1 antibody Dystrophy associated fer 1 like protein antibody Dystrophy associated fer1 like 1 antibody Dystrophy associated fer1 like protein antibody Dystrophy-associated fer-1-like protein antibody Fer 1 like protein 1 antibody Fer-1-like protein 1 antibody Fer1 like protein 1 antibody FER1L1 antibody FLJ00175 antibody FLJ90168 antibody LGMD 2B antibody LGMD2B antibody Limb girdle muscular dystrophy 2B (autosomal recessive) antibody Limb girdle muscular dystrophy 2B antibody Miyoshi myopathy antibody MM antibody MMD1 antibody
Concentration:1 mg/mL.
Clonality:Rabbit polyc
conjugation :Non-conjugated
price :Consultar
format :Liquid
immunogen :Recombinant protein within Human Dysferlin aa 124-31
reactivity :Human
Application:WB,IHC-P,FC
description :The most intensively studied role for dysferlin is in a cellular process called membrane repair. Membrane repair is a critical mechanism by which cells are able to seal dramatic wounds to the plasma membrane. Muscle is thought to be particularly prone to
Cell localization :Plasma membrane, Cytoplasmic vesicle.
isotype :IgG
Positive control :Human fetal skeletal muscle tissue lysate, human kidney tissue, human placenta tissue, human fetal skeletal muscle tissue, HUVEC.
Storage conditions :Store at +4? after thawing. Aliquot store at -20? or -80?. Avoid repeated freeze / thaw cycles.
Simple dilution :WB: 1:500-1:2,000 ;IHC-P: 1:50-1:200 ;FC: 1:50-1:100
buffer :1*PBS (pH7.4), 0.2% BSA, 50% Glycerol. Preservative: 0.05% Sodium Azide.
purity :Immunogen affinity purified.
Molecular weight :Predicted band size: 237 kDa
Uniprot number :SwissProt: O75923 Human


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