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Antibody

Anti-Dysferlin Antibody [JF05-54]

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DESCRIPCIÓN

Supplier:Huabio
Reference:ET1702-45
Name:Anti-Dysferlin Antibody [JF05-54]
Category:Antibody
Subcategory:Primary antibodies
Aditional Names:DMAT antibody DYSF antibody DYSF_HUMAN antibody Dysferlin antibody Dysferlin limb girdle muscular dystrophy 2B (autosomal recessive) antibody Dysferlin limb girdle muscular dystrophy 2B antibody Dystrophy associated fer 1 like 1 antibody Dystrophy associated fer 1 like protein antibody Dystrophy associated fer1 like 1 antibody Dystrophy associated fer1 like protein antibody Dystrophy-associated fer-1-like protein antibody Fer 1 like protein 1 antibody Fer-1-like protein 1 antibody Fer1 like protein 1 antibody FER1L1 antibody FLJ00175 antibody FLJ90168 antibody LGMD 2B antibody LGMD2B antibody Limb girdle muscular dystrophy 2B (autosomal recessive) antibody Limb girdle muscular dystrophy 2B antibody Miyoshi myopathy antibody MM antibody MMD1 antibody
Concentration:1 mg/mL.
Clonality:Recombinant
conjugation :Non-conjugated
price :Consultar
format :Liquid
immunogen :Synthetic peptide within Human Dysferlin aa 113-162
reactivity :Human, Mouse
Application:WB,IF-Cell,IF-Tissue,IHC-P
description :Dysferlin is a muscle-specific protein that is essential for normal muscle function and development. Mutations in the human dysferlin gene, DYSF, which maps to chromosome 2p13.2, are associated with limb girdle muscular dystrophy-2B (LGMD-2B) and a relate
Cell localization :Cell membrane, Cytoplasmic vesicle membrane.
isotype :IgG
Positive control :Skeletal muscle tissue lysates, SW480, human spleen tissue, mouse skeletal muscle tissue, mouse spleen tissue, mouse heart tissue.
Storage conditions :Store at +4? after thawing. Aliquot store at -20? or -80?. Avoid repeated freeze / thaw cycles.
Simple dilution :WB: 1:1,000-1:5,000;IF-Cell: 1:50-1:200;IF-Tissue: 1:50-1:200;IHC-P: 1:50-1:200
buffer :1*TBS (pH7.4), 0.05% BSA, 40% Glycerol. Preservative: 0.05% Sodium Azide.
purity :Protein A affinity purified.
Molecular weight :237 kDa
Uniprot number :SwissProt: O75923 Human;SwissProt: Q9ESD7 Mouse


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