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Antibody

Anti-MYH2 Antibody [JE53-30]

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DESCRIPCIÓN

Supplier:Huabio
Reference:HA721862
Name:Anti-MYH2 Antibody [JE53-30]
Category:Antibody
Subcategory:Primary antibodies
Aditional Names:adult 2 antibody Fast 2a myosin heavy chain antibody IBM3 antibody Inclusion body myopathy 3, autosomal dominant antibody MYH2 antibody MYH2_HUMAN antibody MYH2A antibody MYHas8 antibody MyHC IIa antibody MyHC-2a antibody MyHC-IIa antibody MYHSA2 antibody Myosin heavy chain 2 antibody Myosin heavy chain 2a antibody Myosin heavy chain antibody Myosin heavy chain IIa antibody Myosin heavy chain skeletal muscle adult 2 antibody Myosin heavy polypeptide 2 skeletal muscle adult antibody Myosin-2 antibody MYPOP antibody skeletal muscle antibody Type IIA myosin heavy chain antibody
Concentration:1 mg/ml
Clonality:Recombinant
conjugation :Non-conjugated
price :Consultar
format :Liquid
immunogen :Synthetic peptide within Human MYH2 aa 50-150.
reactivity :Human, Mouse, Rat
Application:WB,IHC-P
description :Defects in MYH2 are the cause of inclusion body myopathy type 3 (IBM3) [MIM:605637]. Hereditary inclusion body myopathies constitute a group of neuromuscular disorders characterized by slowly progressive distal and proximal weakness and a typical muscle p
Cell localization :Cytoplasm.
isotype :IgG
Positive control :Mouse skeletal muscle tissue lysate, rat skeletal muscle tissue lysate, human skeletal muscle tissue, mouse skeletal muscle tissue, rat skeletal muscle tissue.
Storage conditions :Store at +4? after thawing. Aliquot store at -20?. Avoid repeated freeze / thaw cycles.
Simple dilution :WB: 1:1,000 ;IHC-P: 1:5,000
buffer :1*TBS (pH7.4), 0.05% BSA, 40% Glycerol. Preservative: 0.05% Sodium Azide.
purity :Protein A affinity purified.
Molecular weight :Predicted band size: 223 kDa
Uniprot number :SwissProt: Q9UKX2 Human;SwissProt: Q5SX41 Mouse;SwissProt: Q07443 Rat


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